chapter 1 Normal Development of the Ear In the Human and Mouse / chapter 2 Audiometric Tests and Diagnostic Workup / chapter 3 Classification and Epidemiology / chapter 4 Usher Syndrome / chapter 5 Pendred Syndrome -- chapter 6 Waardenburg Syndrome / chapter 7 Jervell and Lange-Nielsen Syndrome / chapter 8 HDR Syndrome / chapter 9 Branchio-oto-renal Syndrome / chapter 10 Treacher Collins Syndrome / chapter 11 MYH9 / chapter 12 Mitochondrial Hearing Loss / chapter 13 Gene Localization and Isolation in Nonsyndromic Hearing Loss / chapter 14 Connexins / chapter 15 Myosin VI / chapter 16 K +-Channel Gene KCNQ4 -- chapter 17 COL11A2 -- chapter 18 POU-Domain Transcription Factors / chapter 19a-Tectorin -- chapter 20 EYA4 -- chapter 21 DFNA5 -- chapter 22 COCH -- chapter 23 Diaphanous / chapter 24 Claudin 14 -- chapter 25 CDH23 -- chapter 26 TMPRSS3 -- chapter 27 Otosclerosis / chapter 28 Mechanisms that Regulate Hair Cell Differentiation and Regeneration -- chapter 29 Genetic Testing: Possibilities and Attitudes